The Experts below are selected from a list of 78 Experts worldwide ranked by ideXlab platform
Jerry Shapiro - One of the best experts on this subject based on the ideXlab platform.
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Primary cicatricial Alopecia: Other lymphocytic primary cicatricial Alopecias and neutrophilic and mixed primary cicatricial Alopecias
Journal of The American Academy of Dermatology, 2016Co-Authors: Chantal Bolduc, Leonard C. Sperling, Jerry ShapiroAbstract:Primary cicatricial Alopecias can be frustrating for both patients and physicians. Proper diagnosis guides more successful management of these challenging conditions. Part II will cover the remaining lymphocytic primary cicatricial Alopecias, which include pseudopelade of Brocq, central centrifugal cicatricial Alopecia, Alopecia Mucinosa, and keratosis follicularis spinulosa decalvans. It will also discuss the neutrophilic and mixed primary cicatricial Alopecias, namely folliculitis decalvans, dissecting cellulitis, folliculitis keloidalis, folliculitis (acne) necrotica, and erosive pustular dermatosis.
Rego, Prisco Medeiros De Melo - One of the best experts on this subject based on the ideXlab platform.
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Follicular mucinosis: literature review and case report
Sociedade Brasileira de Dermatologia, 2002Co-Authors: Fonseca, Antônio De Pádua Marques Da, Bona, Sebastião Honório, Wanda Silveira M. Da ,fonseca, Campelo, Francisco Soares, Rego, Prisco Medeiros De MeloAbstract:A mucinose follicular (MuF), também chamada de Alopecia Mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada a diversos processos benignos e malignos. Os autores apresentam um caso de mucinose folicular primária e fazem breve revisão do assunto. Trata-se de uma paciente de 26 anos de idade, com placa eritematosa recoberta por fina descamação, alopécica e localizada no supercílio direito. Após seis meses, sem qualquer tratamento, houve resolução espontânea da lesão. A paciente permaneceu durante 12 meses em controle ambulatorial sem que se evidenciasse qualquer sinal de recidiva.Follicular mucinosis, also known as Alopecia Mucinosa, is a cutaneous mucinosis characterized by mucin accumulation predominantly in the pilosebaceous follicle. Two forms are distinguished: an idiopathic, or primary form, which is benign and without associated disease, and a symptomatic form associated with lymphoproliferative disorder, most commonly the cutaneous T-cell lymphoma mycosis fungoides. The authors present a new case of the disease and a brief review of the literature. The patient was a 26-year-old female with an asymptomatic plaque of erythema and scaling with Alopecia on her right eyebrow. The lesion resolved spontaneously six months later. We have followed the patient over twelve months without relapse
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Mucinose Folicular: revisão da literatura e relato de um caso
Sociedade Brasileira de Dermatologia, 2002Co-Authors: Fonseca, Antônio De Pádua Marques Da, Bona, Sebastião Honório, Wanda Silveira M. Da ,fonseca, Campelo, Francisco Soares, Rego, Prisco Medeiros De MeloAbstract:A mucinose follicular (MuF), também chamada de Alopecia Mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada a diversos processos benignos e malignos. Os autores apresentam um caso de mucinose folicular primária e fazem breve revisão do assunto. Trata-se de uma paciente de 26 anos de idade, com placa eritematosa recoberta por fina descamação, alopécica e localizada no supercílio direito. Após seis meses, sem qualquer tratamento, houve resolução espontânea da lesão. A paciente permaneceu durante 12 meses em controle ambulatorial sem que se evidenciasse qualquer sinal de recidiva
Chantal Bolduc - One of the best experts on this subject based on the ideXlab platform.
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Primary cicatricial Alopecia: Other lymphocytic primary cicatricial Alopecias and neutrophilic and mixed primary cicatricial Alopecias
Journal of The American Academy of Dermatology, 2016Co-Authors: Chantal Bolduc, Leonard C. Sperling, Jerry ShapiroAbstract:Primary cicatricial Alopecias can be frustrating for both patients and physicians. Proper diagnosis guides more successful management of these challenging conditions. Part II will cover the remaining lymphocytic primary cicatricial Alopecias, which include pseudopelade of Brocq, central centrifugal cicatricial Alopecia, Alopecia Mucinosa, and keratosis follicularis spinulosa decalvans. It will also discuss the neutrophilic and mixed primary cicatricial Alopecias, namely folliculitis decalvans, dissecting cellulitis, folliculitis keloidalis, folliculitis (acne) necrotica, and erosive pustular dermatosis.
Alex Zvulunov - One of the best experts on this subject based on the ideXlab platform.
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clinical and histopathologic spectrum of Alopecia Mucinosa follicular mucinosis and its natural history in children
Journal of The American Academy of Dermatology, 2012Co-Authors: Alex Zvulunov, Vered Shkalim, Dan Benamitai, Meora FeinmesserAbstract:Background Some authorities consider Alopecia Mucinosa (AM)/follicular mucinosis (FM) to invariably represent mycosis fungoides (MF). This understanding of AM/FM derives from observations in adults. Objectives We sought to explore the clinicopathologic features and natural history of pediatric AM/FM. Methods Medical records were searched for children given the diagnosis of AM/FM from 1998 through 2009. Diagnosis of AM/FM was defined as the presence of well-demarcated hairless plaques with follicular prominence plus an abundance of mucin on histopathologic examination. Results Forty children with a clinical diagnosis of AM/FM were identified. Nine did not meet the inclusion criteria. In the 31 remaining cases (16 boys, 15 girls) the mean age at onset was 9 ± 3.5 years. Histopathologic examination showed folliculotropism in 28 patients (90%) and epidermotropism in 15 (48%). Twelve cases fulfilled the International Society of Cutaneous Lymphomas (ISCL) diagnostic criteria for early MF. The histopathologic findings were typical of MF in only in two of these cases. T-cell receptor gene rearrangement was positive in 3 of 6 (50%) of tested samples, one in a patient who fulfilled the ISCL criteria for early MF. Mean duration of follow-up was 6.2 ± 3.7 years. All skin lesions resolved and none persisted or recurred. Hodgkin lymphoma was diagnosed 6 months after diagnosis of AM/FM in one patient. Limitations This was a retrospective study. Conclusions Although some pediatric cases meet the diagnostic criteria for MF, AM/FM cannot be regarded unequivocally as early follicular MF in this age group. We suggest the current diagnostic criteria for early MF should exclude children with AM/FM. Long-term follow-up of children with AM/FM is nevertheless warranted.
Wanda Silveira M. Da ,fonseca - One of the best experts on this subject based on the ideXlab platform.
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Follicular mucinosis: literature review and case report
Sociedade Brasileira de Dermatologia, 2002Co-Authors: Fonseca, Antônio De Pádua Marques Da, Bona, Sebastião Honório, Wanda Silveira M. Da ,fonseca, Campelo, Francisco Soares, Rego, Prisco Medeiros De MeloAbstract:A mucinose follicular (MuF), também chamada de Alopecia Mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada a diversos processos benignos e malignos. Os autores apresentam um caso de mucinose folicular primária e fazem breve revisão do assunto. Trata-se de uma paciente de 26 anos de idade, com placa eritematosa recoberta por fina descamação, alopécica e localizada no supercílio direito. Após seis meses, sem qualquer tratamento, houve resolução espontânea da lesão. A paciente permaneceu durante 12 meses em controle ambulatorial sem que se evidenciasse qualquer sinal de recidiva.Follicular mucinosis, also known as Alopecia Mucinosa, is a cutaneous mucinosis characterized by mucin accumulation predominantly in the pilosebaceous follicle. Two forms are distinguished: an idiopathic, or primary form, which is benign and without associated disease, and a symptomatic form associated with lymphoproliferative disorder, most commonly the cutaneous T-cell lymphoma mycosis fungoides. The authors present a new case of the disease and a brief review of the literature. The patient was a 26-year-old female with an asymptomatic plaque of erythema and scaling with Alopecia on her right eyebrow. The lesion resolved spontaneously six months later. We have followed the patient over twelve months without relapse
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Mucinose Folicular: revisão da literatura e relato de um caso
Sociedade Brasileira de Dermatologia, 2002Co-Authors: Fonseca, Antônio De Pádua Marques Da, Bona, Sebastião Honório, Wanda Silveira M. Da ,fonseca, Campelo, Francisco Soares, Rego, Prisco Medeiros De MeloAbstract:A mucinose follicular (MuF), também chamada de Alopecia Mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada a diversos processos benignos e malignos. Os autores apresentam um caso de mucinose folicular primária e fazem breve revisão do assunto. Trata-se de uma paciente de 26 anos de idade, com placa eritematosa recoberta por fina descamação, alopécica e localizada no supercílio direito. Após seis meses, sem qualquer tratamento, houve resolução espontânea da lesão. A paciente permaneceu durante 12 meses em controle ambulatorial sem que se evidenciasse qualquer sinal de recidiva
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Mucinose Folicular: revisão da literatura e relato de um caso Follicular mucinosis: literature review and case report
Sociedade Brasileira de Dermatologia, 2002Co-Authors: Antônio De Pádua Marques Da Fonseca, Wanda Silveira M. Da ,fonseca, Sebastião Honório Bona, Francisco Soares Campelo, Prisco Medeiros De Melo RegoAbstract:A mucinose follicular (MuF), também chamada de Alopecia Mucinosa, é mucinose cutânea caracterizada pelo acúmulo de mucina no folículo pilossebáceo. As mucinoses têm duas formas de apresentação: uma idiopática ou primária, e outra sintomática ou associada a diversos processos benignos e malignos. Os autores apresentam um caso de mucinose folicular primária e fazem breve revisão do assunto. Trata-se de uma paciente de 26 anos de idade, com placa eritematosa recoberta por fina descamação, alopécica e localizada no supercílio direito. Após seis meses, sem qualquer tratamento, houve resolução espontânea da lesão. A paciente permaneceu durante 12 meses em controle ambulatorial sem que se evidenciasse qualquer sinal de recidiva.Follicular mucinosis, also known as Alopecia Mucinosa, is a cutaneous mucinosis characterized by mucin accumulation predominantly in the pilosebaceous follicle. Two forms are distinguished: an idiopathic, or primary form, which is benign and without associated disease, and a symptomatic form associated with lymphoproliferative disorder, most commonly the cutaneous T-cell lymphoma mycosis fungoides. The authors present a new case of the disease and a brief review of the literature. The patient was a 26-year-old female with an asymptomatic plaque of erythema and scaling with Alopecia on her right eyebrow. The lesion resolved spontaneously six months later. We have followed the patient over twelve months without relapse