The Experts below are selected from a list of 942 Experts worldwide ranked by ideXlab platform
Arif O. Khan - One of the best experts on this subject based on the ideXlab platform.
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Markedly asymmetric Buphthalmos but without anisometropia in a girl with primary congenital glaucoma
Journal of AAPOS : the official publication of the American Association for Pediatric Ophthalmology and Strabismus, 2013Co-Authors: Dora H. Alharkan, Arif O. KhanAbstract:Amblyogenic anisometropia is common in children with primary congenital glaucoma who have asymmetric Buphthalmos. We report the case of a 6-year-old girl with markedly asymmetric Buphthalmos but without anisometropia. Biometry confirmed that the more buphthalmic eye was longer than the contralateral eye and also had flatter keratometry.
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Conditions that can be Mistaken as Early Childhood Glaucoma
Ophthalmic genetics, 2011Co-Authors: Arif O. KhanAbstract:Primary congenital glaucoma (isolated goniodysgenesis) has classic phenotypic features such as increased measured intraocular pressure, globe enlargement (Buphthalmos) with associated myopia, Descemet membrane tears, corneal haze/scarring with associated astigmatism, iris atrophy, and optic nerve cupping. These signs also occur in developmental glaucoma (anterior segment dysgeneses) with infantile onset. However, similar findings can occur in other pediatric conditions which are sometimes are mistaken as early childhood glaucoma.
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Buphthalmos following systemic steroid treatment.
Journal of Pediatric Ophthalmology & Strabismus, 2006Co-Authors: Sami Al-shahwan, Arif O. KhanAbstract:: Corticosteroid-induced glaucoma is a well-recognized phenomenon in adults, but not children. We describe an infant who developed juvenile glaucoma with Buphthalmos while receiving systemic steroid treatment. The intraocular pressure normalized several months following discontinuation of treatment.
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Buphthalmos in the setting of persistent hyperplastic primary vitreous cataract.
American journal of ophthalmology, 2003Co-Authors: Arif O. KhanAbstract:Abstract Purpose To report a case of unilateral persistent hyperplastic primary vitreous cataract presenting with ipsilateral Buphthalmos. Design Retrospective case report. Methods The patient chart was reviewed, and a relevant literature search was performed. Results A four-month-old child presented with persistent hyperplastic primary vitreous cataract in the right eye and ipsilateral Buphthalmos with no discernable angle abnormalities. He underwent lensectomy, anterior vitrectomy, and limited transscleral diode cyclodestruction in the right eye. Conclusions This appears to be the first report of Buphthalmos presenting with unilateral persistent hyperplastic primary vitreous. Despite two comorbidities, the patient has thus far responded well to initial treatment and visual rehabilitation.
Patrick D. Barnes - One of the best experts on this subject based on the ideXlab platform.
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Sturge-Weber syndrome with posterior fossa involvement.
AJNR. American journal of neuroradiology, 1994Co-Authors: Thomas Decker, Kendall M. Jones, Patrick D. BarnesAbstract:Sturge-Weber syndrome, encephalotrigeminal angiomatosis, is a neurocutaneous disorder char acterized by a facial cutaneous vascular nevus, seizures, mental retardation, hemiplegia, hom onymous hemianopia, and Buphthalmos or glau coma (1). The clinical findings are related to vascular anomalies of the face, ocular choroid, and leptomeninges. The imaging findings in Sturge-Weber syndrome may include cerebral calcifications, cerebral atrophy, choroid plexus anomalies, pial and/ or cortical enhancement, and prominent deep-draining veins. The leptomenin geal vascular anomaly is usually located in the anterior occipital, posterior parietal, and temporal cerebrum.
Thomas Decker - One of the best experts on this subject based on the ideXlab platform.
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Sturge-Weber syndrome with posterior fossa involvement.
AJNR. American journal of neuroradiology, 1994Co-Authors: Thomas Decker, Kendall M. Jones, Patrick D. BarnesAbstract:Sturge-Weber syndrome, encephalotrigeminal angiomatosis, is a neurocutaneous disorder char acterized by a facial cutaneous vascular nevus, seizures, mental retardation, hemiplegia, hom onymous hemianopia, and Buphthalmos or glau coma (1). The clinical findings are related to vascular anomalies of the face, ocular choroid, and leptomeninges. The imaging findings in Sturge-Weber syndrome may include cerebral calcifications, cerebral atrophy, choroid plexus anomalies, pial and/ or cortical enhancement, and prominent deep-draining veins. The leptomenin geal vascular anomaly is usually located in the anterior occipital, posterior parietal, and temporal cerebrum.
Kendall M. Jones - One of the best experts on this subject based on the ideXlab platform.
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Sturge-Weber syndrome with posterior fossa involvement.
AJNR. American journal of neuroradiology, 1994Co-Authors: Thomas Decker, Kendall M. Jones, Patrick D. BarnesAbstract:Sturge-Weber syndrome, encephalotrigeminal angiomatosis, is a neurocutaneous disorder char acterized by a facial cutaneous vascular nevus, seizures, mental retardation, hemiplegia, hom onymous hemianopia, and Buphthalmos or glau coma (1). The clinical findings are related to vascular anomalies of the face, ocular choroid, and leptomeninges. The imaging findings in Sturge-Weber syndrome may include cerebral calcifications, cerebral atrophy, choroid plexus anomalies, pial and/ or cortical enhancement, and prominent deep-draining veins. The leptomenin geal vascular anomaly is usually located in the anterior occipital, posterior parietal, and temporal cerebrum.
S Rumelt - One of the best experts on this subject based on the ideXlab platform.
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Congenital unilateral Buphthalmos in Walker-Warburg syndrome: a clinicopathological study.
Eye, 1999Co-Authors: U Rehany, Z I Segal, S RumeltAbstract:Background and purpose Walker-Warburg syndrome is a congenital autosomal recessive oculocerebral disorder characterised by hydrocephalus, brain agyria, microphthalmos and retinal dysplasia with or without meningoencephalocele. We describe an unusual finding of congenital unilateral glaucoma and Buphthalmos in one eye and microphthalmos in the fellow eye of two neonates with Walker-Warburg syndrome. Patients Two neonates with Walker-Warburg syndrome and unusual findings of Buphthalmos in one eye and a microphthalmic fellow eye are presented. Results Histological examination of the buphthalmic eyes revealed the presence of mesenchymal tissue in the anterior angle covered by endothelium. No anterior chamber angle was identified in the microphthalmic fellow eye and the iris was adherent to the corneal periphery. Conclusions Congenital Buphthalmos may also appear in Walker-Warburg syndrome. The Buphthalmos may result from later embryonal ocular developmental arrest than that of the microphthalmic eye.
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Congenital unilateral Buphthalmos in Walker-Warburg syndrome: a clinicopathological study.
Eye (London England), 1999Co-Authors: U Rehany, Z I Segal, S RumeltAbstract:Walker-Warburg syndrome is a congenital autosomal recessive oculocerebral disorder characterised by hydrocephalus, brain agyria, microphthalmos and retinal dysplasia with or without meningoencephalocele. We describe an unusual finding of congenital unilateral glaucoma and Buphthalmos in one eye and microphthalmos in the fellow eye of two neonates with Walker-Warburg syndrome. Two neonates with Walker-Warburg syndrome and unusual findings of Buphthalmos in one eye and a microphthalmic fellow eye are presented. Histological examination of the buphthalmic eyes revealed the presence of mesenchymal tissue in the anterior angle covered by endothelium. No anterior chamber angle was identified in the microphthalmic fellow eye and the iris was adherent to the corneal periphery. Congenital Buphthalmos may also appear in Walker-Warburg syndrome. The Buphthalmos may result from later embryonal ocular developmental arrest than that of the microphthalmic eye.
