The Experts below are selected from a list of 186 Experts worldwide ranked by ideXlab platform
Chuenbin Jiang - One of the best experts on this subject based on the ideXlab platform.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chuenbin JiangAbstract:Rationale: Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chyonghsin Hsu, Hungchang Lee, Shuanpei Lin, Chuenbin JiangAbstract:Rationale Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy. Patient concerns A 4-year-old Taiwanese male patient with MD was referred to the hospital and presented with a palpable epigastric mass. Diagnoses On the basis of the findings of ultrasonography and enhanced computed tomography, the diagnosis was retroperitoneal hematoma. Interventions Interventions included laparotomy with evacuation of the hematoma, manual compression, and suture of the bleeding vessels. Outcomes There were no postoperative complications. Lessons This case emphasizes that bleeding in patients with MD is possible at any site in the body owing to the unstable structure of the connective tissues. Timely diagnosis with proper imaging studies can lead to prompt and appropriate management and save patients from this life-threatening condition.
Chiahuei Peng - One of the best experts on this subject based on the ideXlab platform.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chuenbin JiangAbstract:Rationale: Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chyonghsin Hsu, Hungchang Lee, Shuanpei Lin, Chuenbin JiangAbstract:Rationale Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy. Patient concerns A 4-year-old Taiwanese male patient with MD was referred to the hospital and presented with a palpable epigastric mass. Diagnoses On the basis of the findings of ultrasonography and enhanced computed tomography, the diagnosis was retroperitoneal hematoma. Interventions Interventions included laparotomy with evacuation of the hematoma, manual compression, and suture of the bleeding vessels. Outcomes There were no postoperative complications. Lessons This case emphasizes that bleeding in patients with MD is possible at any site in the body owing to the unstable structure of the connective tissues. Timely diagnosis with proper imaging studies can lead to prompt and appropriate management and save patients from this life-threatening condition.
Poonkiat Suchonwanit - One of the best experts on this subject based on the ideXlab platform.
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Parietal scalp is another affected area in female pattern Hair loss: an analysis of Hair density and Hair diameter.
Clinical cosmetic and investigational dermatology, 2017Co-Authors: Salinee Rojhirunsakool, Poonkiat SuchonwanitAbstract:Purpose Female pattern Hair loss (FPHL) is a common Hair Disease. However, studies of the quantitative measurement of FPHL are still limited. The aim of this study was to investigate the characteristics of Hair density and Hair diameter in normal women and FPHL patients, and further correlate the quantitative measurement with the clinical presentation of FPHL. Patients and methods An evaluation of 471 FPHL patients and 236 normal women was carried out according to the Ludwig classification, and analysis was performed by using a com-puterized handheld USB camera with computer-assisted software. Various areas of the scalp, including frontal, parietal, midscalp, and occipital, were analyzed for Hair density, non-vellus Hair diameter, and percentage of miniaturized Hair. Results The Hair density in normal women was the highest and the lowest in the midscalp and parietal areas, respectively. The FPHL group revealed the lowest Hair density in the parietal area. Significant differences in Hair density, non-vellus Hair diameter, and percentage of miniaturized Hair between the normal and FPHL groups were observed, especially in the midscalp and parietal areas. Conclusion The parietal area is another important affected area in FPHL in addition to the midscalp area. This finding provides novel important information of FPHL and will be useful for Hair transplant surgeons choosing the optimal donor sites for Hair transplantation in women.
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Parietal scalp is another affected area in female pattern Hair loss: an analysis of Hair density and Hair diameter.
Clinical cosmetic and investigational dermatology, 2017Co-Authors: Salinee Rojhirunsakool, Poonkiat SuchonwanitAbstract:Female pattern Hair loss (FPHL) is a common Hair Disease. However, studies of the quantitative measurement of FPHL are still limited. The aim of this study was to investigate the characteristics of Hair density and Hair diameter in normal women and FPHL patients, and further correlate the quantitative measurement with the clinical presentation of FPHL. An evaluation of 471 FPHL patients and 236 normal women was carried out according to the Ludwig classification, and analysis was performed by using a com-puterized handheld USB camera with computer-assisted software. Various areas of the scalp, including frontal, parietal, midscalp, and occipital, were analyzed for Hair density, non-vellus Hair diameter, and percentage of miniaturized Hair. The Hair density in normal women was the highest and the lowest in the midscalp and parietal areas, respectively. The FPHL group revealed the lowest Hair density in the parietal area. Significant differences in Hair density, non-vellus Hair diameter, and percentage of miniaturized Hair between the normal and FPHL groups were observed, especially in the midscalp and parietal areas. The parietal area is another important affected area in FPHL in addition to the midscalp area. This finding provides novel important information of FPHL and will be useful for Hair transplant surgeons choosing the optimal donor sites for Hair transplantation in women.
Waitao Chan - One of the best experts on this subject based on the ideXlab platform.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chuenbin JiangAbstract:Rationale: Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chyonghsin Hsu, Hungchang Lee, Shuanpei Lin, Chuenbin JiangAbstract:Rationale Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy. Patient concerns A 4-year-old Taiwanese male patient with MD was referred to the hospital and presented with a palpable epigastric mass. Diagnoses On the basis of the findings of ultrasonography and enhanced computed tomography, the diagnosis was retroperitoneal hematoma. Interventions Interventions included laparotomy with evacuation of the hematoma, manual compression, and suture of the bleeding vessels. Outcomes There were no postoperative complications. Lessons This case emphasizes that bleeding in patients with MD is possible at any site in the body owing to the unstable structure of the connective tissues. Timely diagnosis with proper imaging studies can lead to prompt and appropriate management and save patients from this life-threatening condition.
Chunyan Yeung - One of the best experts on this subject based on the ideXlab platform.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chuenbin JiangAbstract:Rationale: Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy.
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spontaneous retroperitoneal hemorrhage in menkes Disease a rare case report
Medicine, 2018Co-Authors: Chiahuei Peng, Waitao Chan, Nienlu Wang, Chunyan Yeung, Chyonghsin Hsu, Hungchang Lee, Shuanpei Lin, Chuenbin JiangAbstract:Rationale Menkes Disease (MD), also known as Menkes kinky Hair Disease, is a fatal neurodegenerative Disease caused by a defect in copper metabolism. The symptoms involve multiple organ systems, such as the brain, lung, gastrointestinal tract, urinary tract, connective tissue, and skin. There is currently no cure for this Disease entity, and patients with the classic form of MD usually die from complications between 6 months and 3 years of age. Intracranial hemorrhage secondary to tortuous intracranial arteries is a well-known complication of MD, but spontaneous retroperitoneal hemorrhage, to the best of our knowledge, has never been reported in a patient with MD. Herein, we describe the first case of retroperitoneal hematoma as a complication of MD in a 4-year-old boy. Patient concerns A 4-year-old Taiwanese male patient with MD was referred to the hospital and presented with a palpable epigastric mass. Diagnoses On the basis of the findings of ultrasonography and enhanced computed tomography, the diagnosis was retroperitoneal hematoma. Interventions Interventions included laparotomy with evacuation of the hematoma, manual compression, and suture of the bleeding vessels. Outcomes There were no postoperative complications. Lessons This case emphasizes that bleeding in patients with MD is possible at any site in the body owing to the unstable structure of the connective tissues. Timely diagnosis with proper imaging studies can lead to prompt and appropriate management and save patients from this life-threatening condition.
