The Experts below are selected from a list of 87 Experts worldwide ranked by ideXlab platform
Hongsheng Wang - One of the best experts on this subject based on the ideXlab platform.
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diffuse multibacillary leprosy patient with lucio s phenomenon and positive anticardiolipin antibody misdiagnosed as Lupus Erythematosus Panniculitis in the people s republic of china
Infection and Drug Resistance, 2019Co-Authors: Wei Gao, Zhiming Chen, Haiqin Jiang, Ying Shi, Wenyue Zhang, Hongsheng WangAbstract:Lucio's phenomenon (LP) is a special reactional state associated with diffuse multibacillary leprosy; both exhibit a limitative global distribution mainly in Mexico and Central America. We report a case of a 28-year-old female leprosy patient in the People's Republic of China, together with LP and positive anticardiolipin antibody, characterized by vascular thrombosis and invasion of blood vessel walls by leprosy bacilli, causing extensive skin ulcers and followed by a large number of atrophic scars.
Wei Gao - One of the best experts on this subject based on the ideXlab platform.
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diffuse multibacillary leprosy patient with lucio s phenomenon and positive anticardiolipin antibody misdiagnosed as Lupus Erythematosus Panniculitis in the people s republic of china
Infection and Drug Resistance, 2019Co-Authors: Wei Gao, Zhiming Chen, Haiqin Jiang, Ying Shi, Wenyue Zhang, Hongsheng WangAbstract:Lucio's phenomenon (LP) is a special reactional state associated with diffuse multibacillary leprosy; both exhibit a limitative global distribution mainly in Mexico and Central America. We report a case of a 28-year-old female leprosy patient in the People's Republic of China, together with LP and positive anticardiolipin antibody, characterized by vascular thrombosis and invasion of blood vessel walls by leprosy bacilli, causing extensive skin ulcers and followed by a large number of atrophic scars.
E Alessi - One of the best experts on this subject based on the ideXlab platform.
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sclerodermic linear Lupus Panniculitis report of two cases
Dermatology, 2005Co-Authors: Angelo V Marzano, C Tanzi, Ruggero Caputo, E AlessiAbstract:Lupus Erythematosus Panniculitis is a rare disease characterized by deep subcutaneous nodules, most commonly localized on the upper limbs and face. Unique clinical presentations, such as linear configuration or 'overlap' forms between Lupus Erythematosus Panniculitis and localized scleroderma have been reported. We present here the clinical characteristics, course and laboratory findings of 2 patients having linear Lupus Erythematosus Panniculitis with localized scleroderma-like changes. The 2 patients (of the 14 patients with Lupus Erythematosus Panniculitis seen by us since 1990) were females with a young age at the onset of disease (median, 25 years). In 1 case, evolution into systemic Lupus Erythematosus with severe renal involvement occurred whereas the other patient, who had a spontaneous abortion and exhibited anticardiolipin antibodies, should be followed and screened for the emergence of antiphospholipid syndrome. Thus, the clinical behavior of this variant seems to be more aggressive, as compared with the usual course of Lupus Erythematosus Panniculitis, which is considered to be a benign disease, although some reports have suggested that its prognosis is not always favorable. The linear distribution could be the clinical hallmark of such a unique, 'sclerodermic' subset of Lupus Erythematosus Panniculitis.
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Sclerodermic linear Lupus Panniculitis: report of two cases
'S. Karger AG', 2005Co-Authors: Av Marzano, C Tanzi, Ruggero Caputo, E AlessiAbstract:Lupus Erythematosus Panniculitis is a rare disease characterized by deep subcutaneous nodules, most commonly localized on the upper limbs and face. Unique clinical presentations, such as linear configuration or 'overlap' forms between Lupus Erythematosus Panniculitis and localized scleroderma have been reported. We present here the clinical characteristics, course and laboratory findings of 2 patients having linear Lupus Erythematosus Panniculitis with localized scleroderma-like changes. The 2 patients (of the 14 patients with Lupus Erythematosus Panniculitis seen by us since 1990) were females with a young age at the onset of disease (median, 25 years). In 1 case, evolution into systemic Lupus Erythematosus with severe renal involvement occurred whereas the other patient, who had a spontaneous abortion and exhibited anticardiolipin antibodies, should be followed and screened for the emergence of antiphospholipid syndrome. Thus, the clinical behavior of this variant seems to be more aggressive, as compared with the usual course of Lupus Erythematosus Panniculitis, which is considered to be a benign disease, although some reports have suggested that its prognosis is not always favorable. The linear distribution could be the clinical hallmark of such a unique, 'sclerodermic' subset of Lupus Erythematosus Panniculitis. (2005 S. Karger AG, Basel
Spiros Miyakis - One of the best experts on this subject based on the ideXlab platform.
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Cytophagic histiocytic Panniculitis with haemophagocytosis in a patient with familial multiple lipomatosis and review of the literature
Modern Rheumatology, 2012Co-Authors: Matthew Krilis, Spiros MiyakisAbstract:We report a patient with the extremely rare familial multiple lipomatosis syndrome, who developed the uncommon autoimmune disease cytophagic histiocytic Panniculitis, manifested as inflammation of preexisting lipomas. Despite his initial critical condition and unsuccessful treatment with steroids, he responded to cyclosporin and remains well 15 years after diagnosis. In contrast with most previous reports, our patient stays dependent on cyclosporin; repeated attempts of discontinuing or substituting treatment were quickly followed by relapse. Haemophagocytic Panniculitis is considered as a T-cell disorder, but its exact pathophysiological mechanism has not been clarified. Differential diagnosis of cytophagic histiocytic Panniculitis mainly includes malignant histiocytosis, subcutaneous Panniculitis-like T-cell lymphoma (SPTCL) and Lupus Erythematosus Panniculitis (Lupus profundus). We discuss the main clinical features, diagnostic challenges and treatment issues of this usually benign, but at times life-threatening autoimmune condition.
Wenyue Zhang - One of the best experts on this subject based on the ideXlab platform.
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diffuse multibacillary leprosy patient with lucio s phenomenon and positive anticardiolipin antibody misdiagnosed as Lupus Erythematosus Panniculitis in the people s republic of china
Infection and Drug Resistance, 2019Co-Authors: Wei Gao, Zhiming Chen, Haiqin Jiang, Ying Shi, Wenyue Zhang, Hongsheng WangAbstract:Lucio's phenomenon (LP) is a special reactional state associated with diffuse multibacillary leprosy; both exhibit a limitative global distribution mainly in Mexico and Central America. We report a case of a 28-year-old female leprosy patient in the People's Republic of China, together with LP and positive anticardiolipin antibody, characterized by vascular thrombosis and invasion of blood vessel walls by leprosy bacilli, causing extensive skin ulcers and followed by a large number of atrophic scars.
