The Experts below are selected from a list of 138 Experts worldwide ranked by ideXlab platform
Hernández Pardines - One of the best experts on this subject based on the ideXlab platform.
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AN Optic Nerve Tumor IN VON HIPPEL-LINDAU DISEASE, MASQUERADING AS A RETINAL HEMANGIOMA ANGIOMA RETINIANO COMO SÍNDROME MASCARADA DE Tumor DEL NERVIO ÓPTICO EN LA ENFERMEDAD DE VON HIPPEL-LINDAU
2006Co-Authors: España Gregori, Hernández PardinesAbstract:Clinical case: A 35-year-old man with a family history of von Hippel-Lindau disease was diagnosed to have two retinal hemangiomas in the right eye and another in the left eye. The hemangiomas were treated with cryotherapy and laser photocoagulation respectively. Despite apparent good resolution of the retinal lesions, progressive visual loss was observed. An MRI was then performed and showed bilateral Tumoral lesions of the Optic Nerve compatible with a glioma, meningioma or hemangioblastoma. Currently the visual acuity in his right eye is hand movement, and is 0.6 in the left eye. Discussion: The presence of the retinal hemangiomas delayed the diagnosis of an Optic Nerve Tumor in this patient (Arch Soc Esp Oftalmol 2006; 81: 293-296).
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ANGIOMA RETINIANO COMO SÍNDROME MASCARADA DE Tumor DEL NERVIO ÓPTICO EN LA ENFERMEDAD DE VON HIPPEL-LINDAU AN Optic Nerve Tumor IN VON HIPPEL-LINDAU DISEASE, MASQUERADING AS A RETINAL HEMANGIOMA
2006Co-Authors: España Gregori, Hernández PardinesAbstract:Clinical case: A 35-year-old man with a family history of von Hippel-Lindau disease was diagnosed to have two retinal hemangiomas in the right eye and another in the left eye. The hemangiomas were treated with cryotherapy and laser photocoagulation respectively. Despite apparent good resolution of the retinal lesions, progressive visual loss was observed. An MRI was then performed and showed bilateral Tumoral lesions of the Optic Nerve compatible with a glioma, meningioma or hemangioblastoma. Currently the visual acuity in his right eye is hand movement, and is 0.6 in the left eye. Discussion: The presence of the retinal hemangiomas delayed the diagnosis of an Optic Nerve Tumor in this patient (Arch Soc Esp Oftalmol 2006; 81: 293-296).
Sachin M. Salvi - One of the best experts on this subject based on the ideXlab platform.
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Hemangioblastoma of the Optic Nerve
Survey of ophthalmology, 2018Co-Authors: Lindsay A Mcgrath, Hardeep Singh Mudhar, Sachin M. SalviAbstract:Abstract Optic Nerve hemangioblastoma is a rare Tumor that is usually unilateral and most commonly occurs in the context of von Hippel-Lindau disease. Differential diagnosis is based on clinical history and imaging. Magnetic resonance imaging with gadolinium enhancement is the most useful imaging modality as it can reveal flow voids and an absence of dural attachment, differentiating Optic Nerve hemangioblastoma from other more commonly encountered Optic Nerve Tumors. Optic Nerve hemangioblastoma are usually well-circumscribed vascular lesions composed of stromal cells and vascular endothelial cells. These lesions are diagnosed at a mean age of 37 years and can be asymptomatic, but over time, patients may develop reduction in vision, proptosis, and pain. Surgical excision is well described via orbital, transsphenoidal, or transcranial approaches. Given the risks associated with surgery, a stepwise conservative approach is advocated by most clinicians in the absence of severe symptoms. Although uncommon, this Optic Nerve Tumor should be considered in young patients presenting with pain, proptosis, and Optic Nerve pallor, with or without a history of von Hippel-Lindau disease.
Ralph C. Eagle - One of the best experts on this subject based on the ideXlab platform.
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Extraocular extension of unrecognized choroidal melanoma simulating a primary Optic Nerve Tumor: report of two cases.
Ophthalmology, 1999Co-Authors: Carol L. Shields, Maria Carmen M. Santos, Jerry A. Shields, Arun D. Singh, Ralph C. EagleAbstract:Abstract Background Orbital extraocular extension of choroidal melanoma is well known and is usually detected in eyes with medium and large Tumors, but it is very rare with small melanomas. It is particularly unusual for choroidal melanomas of any size to invade the Optic Nerve or its meninges. Design Two case reports. Participants Two patients with small, relatively inconspicuous juxtapapillary pigmented choroidal lesions were referred with the diagnosis of primary Optic Nerve Tumor. Both demonstrated a large nodular Tumor in the meninges of the Optic Nerve, immediately posterior to the globe. Methods Retrospective review of clinical records and histopathology. Results In both cases, orbital magnetic resonance imaging confirmed the presence of a hyperintense enhancing nodular mass near the anterior portion of the Optic Nerve, prompting Optic Nerve biopsy in one case. Subsequent fundus examination disclosed a small juxtapapillary pigmented choroidal lesion measuring 1.0 mm or less in thickness. These observations suggested that the Optic Nerve Tumor might be nodular extraocular extension of a small choroidal melanoma. Modified enucleation was performed in both cases, and histopathologic examination revealed a nodule of malignant melanoma within the meninges that compressed the Optic Nerve and extended extraocularly from a small, relatively inapparent juxtapapillary choroidal melanoma. In both cases, the extraocular component was large and symptomatic, whereas the intraocular component was inconspicuous. Conclusions Small juxtapapillary choroidal melanomas can exhibit prominent extension into the orbit. All patients with orbital Tumors should have careful ophthalmoscopy.
España Gregori - One of the best experts on this subject based on the ideXlab platform.
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AN Optic Nerve Tumor IN VON HIPPEL-LINDAU DISEASE, MASQUERADING AS A RETINAL HEMANGIOMA ANGIOMA RETINIANO COMO SÍNDROME MASCARADA DE Tumor DEL NERVIO ÓPTICO EN LA ENFERMEDAD DE VON HIPPEL-LINDAU
2006Co-Authors: España Gregori, Hernández PardinesAbstract:Clinical case: A 35-year-old man with a family history of von Hippel-Lindau disease was diagnosed to have two retinal hemangiomas in the right eye and another in the left eye. The hemangiomas were treated with cryotherapy and laser photocoagulation respectively. Despite apparent good resolution of the retinal lesions, progressive visual loss was observed. An MRI was then performed and showed bilateral Tumoral lesions of the Optic Nerve compatible with a glioma, meningioma or hemangioblastoma. Currently the visual acuity in his right eye is hand movement, and is 0.6 in the left eye. Discussion: The presence of the retinal hemangiomas delayed the diagnosis of an Optic Nerve Tumor in this patient (Arch Soc Esp Oftalmol 2006; 81: 293-296).
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ANGIOMA RETINIANO COMO SÍNDROME MASCARADA DE Tumor DEL NERVIO ÓPTICO EN LA ENFERMEDAD DE VON HIPPEL-LINDAU AN Optic Nerve Tumor IN VON HIPPEL-LINDAU DISEASE, MASQUERADING AS A RETINAL HEMANGIOMA
2006Co-Authors: España Gregori, Hernández PardinesAbstract:Clinical case: A 35-year-old man with a family history of von Hippel-Lindau disease was diagnosed to have two retinal hemangiomas in the right eye and another in the left eye. The hemangiomas were treated with cryotherapy and laser photocoagulation respectively. Despite apparent good resolution of the retinal lesions, progressive visual loss was observed. An MRI was then performed and showed bilateral Tumoral lesions of the Optic Nerve compatible with a glioma, meningioma or hemangioblastoma. Currently the visual acuity in his right eye is hand movement, and is 0.6 in the left eye. Discussion: The presence of the retinal hemangiomas delayed the diagnosis of an Optic Nerve Tumor in this patient (Arch Soc Esp Oftalmol 2006; 81: 293-296).
F. Hernández Pardines - One of the best experts on this subject based on the ideXlab platform.
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Angioma retiniano como síndrome mascarada de Tumor del nervio óptico en la enfermedad de Von Hippel-Lindau
Archivos de la Sociedad Espanola de Oftalmologia, 2006Co-Authors: M.r. Fons Martínez, E. España Gregori, J. A. Avino Martinez, F. Hernández PardinesAbstract:espanolCaso clinico: Varon de 35 anos con antecedentes familiares de enfermedad de von Hippel-Lindau (VHL) diagnosticado de dos hemangiomas retinianos en ojo derecho (OD) y uno en ojo izquierdo. Las lesiones se trataron con crioterapia en OD y laserterapia en OI. A pesar de una aparente buena evolucion de las lesiones retinianas hubo una progresiva disminucion de la AV. Se realizo RM donde se evidencio lesiones Tumorales del nervio Optico (NO) bilaterales compatibles con glioma, meningioma o hemangioblastoma. Actualmente: AV (OD): movimiento de manos y AV(OI): 0,6. Discusion: La presencia de los hemangiomas retinianos en este paciente hizo retrasar el diagnostico de un Tumor en el NO, infrecuente en esta entidad. EnglishClinical case: A 35-year-old man with a family history of von Hippel-Lindau disease was diagnosed to have two retinal hemangiomas in the right eye and another in the left eye. The hemangiomas were treated with cryotherapy and laser photocoagulation respectively. Despite apparent good resolution of the retinal lesions, progressive visual loss was observed. An MRI was then performed and showed bilateral Tumoral lesions of the Optic Nerve compatible with a glioma, meningioma or hemangioblastoma. Currently the visual acuity in his right eye is hand movement, and is 0.6 in the left eye. Discussion: The presence of the retinal hemangiomas delayed the diagnosis of an Optic Nerve Tumor in this patient.