The Experts below are selected from a list of 294 Experts worldwide ranked by ideXlab platform
Michael Hofbeck - One of the best experts on this subject based on the ideXlab platform.
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Restrictive ventricular septal defect and critical subaortic stenosis in tetralogy of Fallot
Clinical Research in Cardiology, 2010Co-Authors: Gunter Kerst, Renate Kaulitz, L. Sieverding, Christian Apitz, Gerhard Ziemer, Michael HofbeckAbstract:Introduction Tetralogy of Fallot is characterized by a non-restrictive malalignment ventricular septal defect (VSD), an Overriding Aorta and right ventricular outflow tract obstruction resulting from anterior deviation of the infundibular septum. Due to the large VSD, systolic pressures are equal in both ventricles. In rare cases, redundant tricuspid valve tissue may prolapse into the VSD resulting in restriction of the defect size and causing suprasystemic pressure in the right ventricle. Subaortic obstruction by prolapse of the redundant tricuspid tissue into the left ventricular outflow tract, although theoretically possible in this situation, has not been described yet in the literature. Case report We report on a newborn with tetralogy of Fallot presenting with cyanosis and severe arterial hypotension a few hours after birth. Echocardiography revealed redundant hammock-like accessory tricuspid valve tissue almost completely occluding the originally large VSD. Suprasystemic pressure in the right ventricle resulted in protrusion of tricuspid valve tissue across the VSD and thereby caused severe left ventricular outflow tract obstruction. Emergency pulmonary balloon valvuloplasty performed for decompression of the right ventricle, reduced prolapse of tricuspid tissue into the left ventricular outflow tract and resulted in significant improvement of pulmonary and systemic blood flow. Conclusion In tetralogy of Fallot, accessory tricuspid valve tissue may obstruct the VSD as well as the left ventricular outflow tract resulting in a life threatening condition in newborns shortly after birth.
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Restrictive ventricular septal defect and critical subaortic stenosis in tetralogy of Fallot
Clinical Research in Cardiology, 2010Co-Authors: Gunter Kerst, Renate Kaulitz, L. Sieverding, Christian Apitz, Gerhard Ziemer, Michael HofbeckAbstract:Introduction Tetralogy of Fallot is characterized by a non-restrictive malalignment ventricular septal defect (VSD), an Overriding Aorta and right ventricular outflow tract obstruction resulting from anterior deviation of the infundibular septum. Due to the large VSD, systolic pressures are equal in both ventricles. In rare cases, redundant tricuspid valve tissue may prolapse into the VSD resulting in restriction of the defect size and causing suprasystemic pressure in the right ventricle. Subaortic obstruction by prolapse of the redundant tricuspid tissue into the left ventricular outflow tract, although theoretically possible in this situation, has not been described yet in the literature.
Tomohiro Nakamura - One of the best experts on this subject based on the ideXlab platform.
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Surgical correction of tetralogy of Fallot in a 61-year-old patient
General Thoracic and Cardiovascular Surgery, 2012Co-Authors: Hideki Tsubota, Tomohiro NakamuraAbstract:Tetralogy of Fallot (TOF) is a congenital heart disease that is usually diagnosed and treated during infancy. Only 3% of such patients reach the age of 40 without surgery. We describe a 61-year-old woman with uncorrected TOF that was successfully treated by radical surgery. The patient presented with exertional dyspnea, insomnia, and malaise. Echocardiography and cardiac catheterization indicated a dilated, severely hypertrophic right ventricle, ventricular septal defect, an Overriding Aorta, and infundibular stenosis in the right ventricular outflow tract. All symptoms disappeared after full surgical correction, which remains the preferred treatment for adult TOF because it confers long-term survival and an improved quality of life.
Gunter Kerst - One of the best experts on this subject based on the ideXlab platform.
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Restrictive ventricular septal defect and critical subaortic stenosis in tetralogy of Fallot
Clinical Research in Cardiology, 2010Co-Authors: Gunter Kerst, Renate Kaulitz, L. Sieverding, Christian Apitz, Gerhard Ziemer, Michael HofbeckAbstract:Introduction Tetralogy of Fallot is characterized by a non-restrictive malalignment ventricular septal defect (VSD), an Overriding Aorta and right ventricular outflow tract obstruction resulting from anterior deviation of the infundibular septum. Due to the large VSD, systolic pressures are equal in both ventricles. In rare cases, redundant tricuspid valve tissue may prolapse into the VSD resulting in restriction of the defect size and causing suprasystemic pressure in the right ventricle. Subaortic obstruction by prolapse of the redundant tricuspid tissue into the left ventricular outflow tract, although theoretically possible in this situation, has not been described yet in the literature. Case report We report on a newborn with tetralogy of Fallot presenting with cyanosis and severe arterial hypotension a few hours after birth. Echocardiography revealed redundant hammock-like accessory tricuspid valve tissue almost completely occluding the originally large VSD. Suprasystemic pressure in the right ventricle resulted in protrusion of tricuspid valve tissue across the VSD and thereby caused severe left ventricular outflow tract obstruction. Emergency pulmonary balloon valvuloplasty performed for decompression of the right ventricle, reduced prolapse of tricuspid tissue into the left ventricular outflow tract and resulted in significant improvement of pulmonary and systemic blood flow. Conclusion In tetralogy of Fallot, accessory tricuspid valve tissue may obstruct the VSD as well as the left ventricular outflow tract resulting in a life threatening condition in newborns shortly after birth.
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Restrictive ventricular septal defect and critical subaortic stenosis in tetralogy of Fallot
Clinical Research in Cardiology, 2010Co-Authors: Gunter Kerst, Renate Kaulitz, L. Sieverding, Christian Apitz, Gerhard Ziemer, Michael HofbeckAbstract:Introduction Tetralogy of Fallot is characterized by a non-restrictive malalignment ventricular septal defect (VSD), an Overriding Aorta and right ventricular outflow tract obstruction resulting from anterior deviation of the infundibular septum. Due to the large VSD, systolic pressures are equal in both ventricles. In rare cases, redundant tricuspid valve tissue may prolapse into the VSD resulting in restriction of the defect size and causing suprasystemic pressure in the right ventricle. Subaortic obstruction by prolapse of the redundant tricuspid tissue into the left ventricular outflow tract, although theoretically possible in this situation, has not been described yet in the literature.
Etam Z Zimmer - One of the best experts on this subject based on the ideXlab platform.
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prenatal diagnosis of ventricular septal defect and Overriding Aorta at 14 weeks gestation using trans vaginal sonography
Prenatal Diagnosis, 1990Co-Authors: Moshe Bronshtein, Efraim Siegler, Nechemia Yoffe, Etam Z ZimmerAbstract:Two fetuses with heart abnormalities were detected by transvaginal sonography at 14 weeks of gestation. In the first fetus, a ventricular septal defect and an Overriding Aorta were detected and a diagnosis of tetralogy of Fallot was suggested. In addition, cystic hygroma and omphalocoele were visualized and the cytogenetic study revealed trisomy 18. In the second fetus, ventricular septal defect, pericardial effusion, and omphalocoele were detected.
Hideki Tsubota - One of the best experts on this subject based on the ideXlab platform.
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Surgical correction of tetralogy of Fallot in a 61-year-old patient
General Thoracic and Cardiovascular Surgery, 2012Co-Authors: Hideki Tsubota, Tomohiro NakamuraAbstract:Tetralogy of Fallot (TOF) is a congenital heart disease that is usually diagnosed and treated during infancy. Only 3% of such patients reach the age of 40 without surgery. We describe a 61-year-old woman with uncorrected TOF that was successfully treated by radical surgery. The patient presented with exertional dyspnea, insomnia, and malaise. Echocardiography and cardiac catheterization indicated a dilated, severely hypertrophic right ventricle, ventricular septal defect, an Overriding Aorta, and infundibular stenosis in the right ventricular outflow tract. All symptoms disappeared after full surgical correction, which remains the preferred treatment for adult TOF because it confers long-term survival and an improved quality of life.
