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Hossein C Nousari - One of the best experts on this subject based on the ideXlab platform.

  • hypocomplementemic Urticarial Vasculitis report of a 12 year old girl with systemic lupus erythematosus
    Journal of The American Academy of Dermatology, 2002
    Co-Authors: Tracy Deamicis, Mona Z Mofid, Bernard A. Cohen, Hossein C Nousari
    Abstract:

    Abstract Urticarial Vasculitis, a form of leukocytoclastic Vasculitis involving the postcapillary venules, is classified as a type III hypersensitivity reaction and has been associated with connective tissue disease. The lesions resemble urticaria and typically persist for more than 24 hours. Urticarial Vasculitis usually affects young women, and the diagnosis is confirmed at histologic examination. Patients with Urticarial Vasculitis can be divided into 2 types—those with normal complement levels and those with hypocomplementemic Urticarial Vasculitis (HUV). Patients with normocomplementemic Urticarial Vasculitis have a milder course than do patients with HUV, a condition that has a strong association with systemic lupus erythematosus. Angioedema, ocular inflammation, obstructive lung disease, and glomerulonephritis are commonly associated with HUV. We describe the case of a girl with systemic lupus erythematosus and HUV who also had pancreatitis, hypothyroidism, and elevated levels of antiphospholipid antibodies. (J Am Acad Dermatol 2002;47:S273-4.)

  • Hypocomplementemic Urticarial Vasculitis: report of a 12-year-old girl with systemic lupus erythematosus.
    Journal of the American Academy of Dermatology, 2002
    Co-Authors: Tracy Deamicis, Mona Z Mofid, Bernard Cohen, Hossein C Nousari
    Abstract:

    Urticarial Vasculitis, a form of leukocytoclastic Vasculitis involving the postcapillary venules, is classified as a type III hypersensitivity reaction and has been associated with connective tissue disease. The lesions resemble urticaria and typically persist for more than 24 hours. Urticarial Vasculitis usually affects young women, and the diagnosis is confirmed at histologic examination. Patients with Urticarial Vasculitis can be divided into 2 types--those with normal complement levels and those with hypocomplementemic Urticarial Vasculitis (HUV). Patients with normocomplementemic Urticarial Vasculitis have a milder course than do patients with HUV, a condition that has a strong association with systemic lupus erythematosus. Angioedema, ocular inflammation, obstructive lung disease, and glomerulonephritis are commonly associated with HUV. We describe the case of a girl with systemic lupus erythematosus and HUV who also had pancreatitis, hypothyroidism, and elevated levels of antiphospholipid antibodies.

  • Hypocomplementemic Urticarial Vasculitis: Report of a 12-year-old girl with systemic lupus erythematosus ☆ ☆☆
    Journal of the American Academy of Dermatology, 2002
    Co-Authors: Tracy Deamicis, Mona Z Mofid, Bernard A. Cohen, Hossein C Nousari
    Abstract:

    Abstract Urticarial Vasculitis, a form of leukocytoclastic Vasculitis involving the postcapillary venules, is classified as a type III hypersensitivity reaction and has been associated with connective tissue disease. The lesions resemble urticaria and typically persist for more than 24 hours. Urticarial Vasculitis usually affects young women, and the diagnosis is confirmed at histologic examination. Patients with Urticarial Vasculitis can be divided into 2 types—those with normal complement levels and those with hypocomplementemic Urticarial Vasculitis (HUV). Patients with normocomplementemic Urticarial Vasculitis have a milder course than do patients with HUV, a condition that has a strong association with systemic lupus erythematosus. Angioedema, ocular inflammation, obstructive lung disease, and glomerulonephritis are commonly associated with HUV. We describe the case of a girl with systemic lupus erythematosus and HUV who also had pancreatitis, hypothyroidism, and elevated levels of antiphospholipid antibodies. (J Am Acad Dermatol 2002;47:S273-4.)

Osman Sener - One of the best experts on this subject based on the ideXlab platform.

  • Plasmapheresis in a Patient With "Refractory" Urticarial Vasculitis
    Allergy asthma & immunology research, 2012
    Co-Authors: Ozgur Kartal, Mustafa Gulec, Z. Caliskaner, Oral Nevruz, Türker Çetin, Osman Sener
    Abstract:

    Immune complexes are found in the circulation of 30%-75% of patients with Urticarial Vasculitis and much evidence supports the role of these immune complexes in the pathogenesis of Urticarial Vasculitis. Plasmapheresis is effective for removing these immune complexes; however, there are few reports on the use of plasmapheresis in the treatment of Urticarial Vasculitis. We describe a case of "refractory" Urticarial Vasculitis in which the symptoms improved after plasmapheresis treatment. We suggest that plasmapheresis be considered as an option in patients with severe or treatment-resistant Urticarial Vasculitis.

  • 587 Plasmapheresis in a Patient with “Refractory” Urticarial Vasculitis
    World Allergy Organization Journal, 2012
    Co-Authors: Ozgur Kartal, Mustafa Gulec, Z. Caliskaner, Oral Nevruz, Türker Çetin, Osman Sener
    Abstract:

    Background Immune complexes have been found in the circulation approximately 30 to 75% of patients with Urticarial Vasculitis and much evidence supports the role of these immune complexes in the pathogenesis of Urticarial Vasculitis. Plasmapheresis is effective in removal of these immune complexes. However, few cases have been reported regarding the use of plasmapheresis in the treatment of Urticarial Vasculitis.

Jeffrey J. Wisnieski - One of the best experts on this subject based on the ideXlab platform.

  • Hypocomplementemic Urticarial Vasculitis syndrome in identical twins
    Arthritis and rheumatism, 1994
    Co-Authors: Jeffrey J. Wisnieski, Steven N. Emancipator, Neil J. Korman, Jonathan H. Lass, Tarif M. Zaim, E. R. Mcfadden
    Abstract:

    Hypocomplementemic Urticarial Vasculitis syndrome (HUVS) is a syndrome of recurrent Urticarial Vasculitis, arthralgia/arthritis, and hypocomplementemia. Angioedema, ocular inflammation, glomerulonephritis, and obstructive lung disease are other clinical findings. Although the etiology of HUVS is unknown, its resemblance to systemic lupus erythematosus (SLE) suggests a similar pathogenesis. SLE is known to occur in identical twins. This is the first report of a pair of identical twins with HUVS. Concordance for HUVS in identical twins suggests that the pathogenesis of the disease involves abnormal genetic immunoregulation.

  • Hypocomplementemic Urticarial Vasculitis syndrome with severe systemic manifestations.
    The Journal of Pediatrics, 1994
    Co-Authors: A Martini, A Ravelli, S Albani, F De Benedetti, M Massa, Jeffrey J. Wisnieski
    Abstract:

    Abstract We describe two children with clinical and laboratory features of hypocomplementemic Urticarial Vasculitis syndrome. Both patients had severe, life-threatening manifestations: rapidly progressive glomerulonephritis (patient 1) and pulmonary hemorrhage (patient 2). We conclude that this syndrome may be a potentially severe multisystem disease. (J PEDIATR 1994;124:742-4)

A Martini - One of the best experts on this subject based on the ideXlab platform.

J. J. Wisnieski - One of the best experts on this subject based on the ideXlab platform.

  • Autoantibodies in systemic lupus erythematosus and Urticarial Vasculitis.
    The Journal of rheumatology, 1995
    Co-Authors: David D'cruz, J. J. Wisnieski, R. A. Asherson, M. A. Khamashta, G. R. V. Hughes
    Abstract:

    Objective. Urticarial Vasculitis (UV) is both a primary disorder and a cutaneous vasculitic manifestation in patients with connective tissue diseases. We examined the prevalence of autoantibodies to vascular endothelial cells (aECA) and anti-C1q antibodies in patients with UV. Methods. ELISA were used to detect aECA and anti-C1q autoantibodies, and we tested for correlation with UV in 4 patient groups : healthy controls, patients with systemic lupus erythematosus (SLE) with and without UV, patients with primary systemic vasculitides with UV, and patients with hypocomplementemic Urticarial Vasculitis syndrome (HUVS). Results. aECA were detected in 82% of patients with SLE with UV and 70% of patients with HUVS. In contrast, aECA were found in 32% of patients with SLE without UV and 14% of patients with primary UV. Anti-Clq antibodies were present in all patients with HUVS, but in

  • Hypocomplementemic Urticarial Vasculitis syndrome with severe systemic manifestations.
    The Journal of pediatrics, 1994
    Co-Authors: A Martini, A Ravelli, S Albani, F De Benedetti, M Massa, J. J. Wisnieski
    Abstract:

    We describe two children with clinical and laboratory features of hypocomplementemic Urticarial Vasculitis syndrome. Both patients had severe, life-threatening manifestations: rapidly progressive glomerulonephritis (patient 1) and pulmonary hemorrhage (patient 2). We conclude that this syndrome may be a potentially severe multisystem disease.