The Experts below are selected from a list of 249 Experts worldwide ranked by ideXlab platform
Terje Terjesen - One of the best experts on this subject based on the ideXlab platform.
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epidemiology and treatment outcome of Congenital Pseudarthrosis of the tibia
Journal of Children's Orthopaedics, 2013Co-Authors: Joachim Horn, Harald Steen, Terje TerjesenAbstract:Purpose Congenital Pseudarthrosis of the tibia (CPT) is a rare disease. Epidemiological data are limited, and treatment of the condition is challenging. The purpose of our study was to gain epidemiological data on the incidence of CPT in Norway and to evaluate the treatment outcome of the disease.
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Epidemiology and treatment outcome of Congenital Pseudarthrosis of the tibia
Journal of children's orthopaedics, 2013Co-Authors: Joachim Horn, Harald Steen, Terje TerjesenAbstract:Purpose Congenital Pseudarthrosis of the tibia (CPT) is a rare disease. Epidemiological data are limited, and treatment of the condition is challenging. The purpose of our study was to gain epidemiological data on the incidence of CPT in Norway and to evaluate the treatment outcome of the disease.
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Residual challenges after healing of Congenital Pseudarthrosis in the tibia
Clinical orthopaedics and related research, 2003Co-Authors: Leif Pål Kristiansen, Harald Steen, Terje TerjesenAbstract:The purpose of the current study was to evaluate the clinical results of the Ilizarov bone transport method in the treatment of Congenital Pseudarthrosis in the tibia. In seven patients operated on between 2.6 and 7.8 years of age, primary healing of the Pseudarthrosis was achieved in all patients (after additional bone grafting in two patients). Within a followup of 6 to 8 years, major complications occurred in all patients. Five refractures occurred, and in one patient the refracture did not heal. At the last followup, axial deformities and an abnormal malalignment test with lateral mechanical axis deviation of 10 mm or greater was found in all patients. Three patients had leg length inequality of 20 mm or more. The Ilizarov bone transport method is useful in achieving primary healing in Congenital Pseudarthrosis of the tibia, but residual challenges with secondary reconstructive surgery caused by refracture and postoperative deformities must be expected.
S. Shivapuri - One of the best experts on this subject based on the ideXlab platform.
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Congenital Pseudarthrosis of radius. A case report
Strategies in Trauma and Limb Reconstruction, 2006Co-Authors: J. Mukhopadhaya, S. ShivapuriAbstract:We report a case of a 9 year old female child with Congenital Pseudarthrosis of the radius. She had a history of fractures of both bones of the left forearm after trivial trauma at the age of 7 years (2003) and 8 years (2004). On each occasion she was treated conservatively in a POP cast 4 weeks. She reported to us in January 2005 complaining of a gradually increasing deformity of the left forearm. Radiologically, it was an apex anterior deformity of the distal aspect of the left radius. Clinically she had multiple cafe au lait spots over her body. Neurological and ophthalmological examinations were normal. The fibrous tissue and the fracture ends were excised. The fracture was stabilized with a 6-hole DCP with iliac crest graft to bridge the gap along with cortico-cancellous chips. The fracture united uneventfully at 3 months post-operatively. At 17 months post-operatively there is no evidence of recurrence of Pseudarthrosis with a near normal range of movements. Congenital Pseudarthrosis of the radius is an extremely rare condition with only 10 cases seems to have been reported. Dual onlay bone graft, vascularised fibular graft has been the treatment options the latter being the preferred one. But the disease being extremely rare not much has been documented about the treatment options. We treated this case by excision of the sclerotic bone ends along with a cuff of periosteum and internal fixation with DCP along with iliac strut graft to restore the length. Successful union was achieved in 3 months and the patient has satisfactory follow-up at 17 months.
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Congenital Pseudarthrosis of radius. A case report
Strategies in Trauma and Limb Reconstruction, 2006Co-Authors: J. Mukhopadhaya, S. ShivapuriAbstract:We report a case of a 9 year old female child with Congenital Pseudarthrosis of the radius. She had a history of fractures of both bones of the left forearm after trivial trauma at the age of 7 years (2003) and 8 years (2004). On each occasion she was treated conservatively in a POP cast 4 weeks. She reported to us in January 2005 complaining of a gradually increasing deformity of the left forearm. Radiologically, it was an apex anterior deformity of the distal aspect of the left radius. Clinically she had multiple café au lait spots over her body. Neurological and ophthalmological examinations were normal. The fibrous tissue and the fracture ends were excised. The fracture was stabilized with a 6-hole DCP with iliac crest graft to bridge the gap along with cortico-cancellous chips. The fracture united uneventfully at 3 months post-operatively. At 17 months post-operatively there is no evidence of recurrence of Pseudarthrosis with a near normal range of movements. Congenital Pseudarthrosis of the radius is an extremely rare condition with only 10 cases seems to have been reported. Dual onlay bone graft, vascularised fibular graft has been the treatment options the latter being the preferred one. But the disease being extremely rare not much has been documented about the treatment options. We treated this case by excision of the sclerotic bone ends along with a cuff of periosteum and internal fixation with DCP along with iliac strut graft to restore the length. Successful union was achieved in 3 months and the patient has satisfactory follow-up at 17 months.
B. Mayou - One of the best experts on this subject based on the ideXlab platform.
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Free vascularised fibular grafts for Congenital Pseudarthrosis of the tibia
The Journal of bone and joint surgery. British volume, 1991Co-Authors: R. B. Simonis, H. R. Shirali, B. MayouAbstract:We describe 11 patients with Congenital Pseudarthrosis of the tibia treated by a free vascularised fibular graft (FVFG) and followed up from 10 to 64 months (mean 38). Bony union was achieved in nine of the 11 cases: two failures required amputation. The mean time for union in the successful cases was five months. Nine of the 11 patients had had an average of four surgical procedures before the FVFG, so the graft was a salvage procedure for which the only alternative was amputation. FVFG is recommended as a primary procedure for the treatment of Congenital Pseudarthrosis of the tibia if there is a large tibial defect (over 3 cm) or shortening of more than 5 cm. The primary use of this operation is not advised for cases in which standard orthopaedic procedures are expected to succeed. For a small defect with a favourable prognosis (Boyd and Sage 1958), we recommend conventional bone grafting, intramedullary nailing and electrical stimulation.
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FREE VASCULARISED FIBULAR GRAVIS FOR Congenital Pseudarthrosis OF THE TIBIA
1991Co-Authors: R. B. Simonis, H. R. Shirali, B. MayouAbstract:We describe 11 patients with Congenital Pseudarthrosis of the tibia treated by a free vascularised fibular graft (FVFG) and followed up from 10 to 64 months (mean 38). Bony union was achieved in nine of the 11 cases: two failures required amputation. The mean time for union in the successful cases was five months. Nine of the 11 patients had had an average of four surgical procedures before the FVFG, so the graft was a salvage procedure for which the only alternative was amputation. FVFG is recommended as a primary procedure for the treatment of Congenital Pseudarthrosis of the tibia if there is a large tibial defect (over 3 cm) or shortening of more than 5 cm, The primary use of this operation is not advised for cases in which standard orthopaedic procedures are expected to succeed. For a small defect with a favourable prognosis (Boyd and Sage 1958), we recommend conventional bone grafting, inframedullary nailing and electrical stimulation.
Heechang Ahn - One of the best experts on this subject based on the ideXlab platform.
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Early Vascularized Fibular Grafts in Infants with Congenital Pseudarthrosis
Archives of plastic surgery, 2016Co-Authors: Ki Ho Kim, Seungki Youn, Tai Seung Kim, Heechang AhnAbstract:Neurofibromatosis type I, also known as Von Recklinghausen disease, is one of the most common Congenital disorders, with an incidence of 1 out of 3,000–4,000. It can be diagnosed on the basis of characteristic phenotypic manifestations, such as cafe-au-lait spots, axillary and inguinal freckling, neurofibromas, optic gliomas, Lisch nodules and distinctive osseous lesions. Osseous lesions occur in 2%–3% of neurofibromatosis type I cases, and are known to be caused by a lack of osteoblast function and the consolidation of osteoclast activity [1]. The most commonly affected region is the diaphysis of the tibia. Due to segmental disturbances in periosteal bone formation, anterior bowing occurs, and pathologic fractures eventually develop. In the first 2 years of life, Pseudarthrosis may occur, which makes bone healing difficult due to persistent instability and progressive deformity in the bone. In patients with Congenital Pseudarthrosis, serious consequences such as amputation of the lower limb may be necessary if the condition is not adequately managed [2]. In this report, the authors describe the case of a vascularized fibular bone graft in a Congenital Pseudarthrosis patient.
J. Mukhopadhaya - One of the best experts on this subject based on the ideXlab platform.
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Congenital Pseudarthrosis of radius. A case report
Strategies in Trauma and Limb Reconstruction, 2006Co-Authors: J. Mukhopadhaya, S. ShivapuriAbstract:We report a case of a 9 year old female child with Congenital Pseudarthrosis of the radius. She had a history of fractures of both bones of the left forearm after trivial trauma at the age of 7 years (2003) and 8 years (2004). On each occasion she was treated conservatively in a POP cast 4 weeks. She reported to us in January 2005 complaining of a gradually increasing deformity of the left forearm. Radiologically, it was an apex anterior deformity of the distal aspect of the left radius. Clinically she had multiple cafe au lait spots over her body. Neurological and ophthalmological examinations were normal. The fibrous tissue and the fracture ends were excised. The fracture was stabilized with a 6-hole DCP with iliac crest graft to bridge the gap along with cortico-cancellous chips. The fracture united uneventfully at 3 months post-operatively. At 17 months post-operatively there is no evidence of recurrence of Pseudarthrosis with a near normal range of movements. Congenital Pseudarthrosis of the radius is an extremely rare condition with only 10 cases seems to have been reported. Dual onlay bone graft, vascularised fibular graft has been the treatment options the latter being the preferred one. But the disease being extremely rare not much has been documented about the treatment options. We treated this case by excision of the sclerotic bone ends along with a cuff of periosteum and internal fixation with DCP along with iliac strut graft to restore the length. Successful union was achieved in 3 months and the patient has satisfactory follow-up at 17 months.
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Congenital Pseudarthrosis of radius. A case report
Strategies in Trauma and Limb Reconstruction, 2006Co-Authors: J. Mukhopadhaya, S. ShivapuriAbstract:We report a case of a 9 year old female child with Congenital Pseudarthrosis of the radius. She had a history of fractures of both bones of the left forearm after trivial trauma at the age of 7 years (2003) and 8 years (2004). On each occasion she was treated conservatively in a POP cast 4 weeks. She reported to us in January 2005 complaining of a gradually increasing deformity of the left forearm. Radiologically, it was an apex anterior deformity of the distal aspect of the left radius. Clinically she had multiple café au lait spots over her body. Neurological and ophthalmological examinations were normal. The fibrous tissue and the fracture ends were excised. The fracture was stabilized with a 6-hole DCP with iliac crest graft to bridge the gap along with cortico-cancellous chips. The fracture united uneventfully at 3 months post-operatively. At 17 months post-operatively there is no evidence of recurrence of Pseudarthrosis with a near normal range of movements. Congenital Pseudarthrosis of the radius is an extremely rare condition with only 10 cases seems to have been reported. Dual onlay bone graft, vascularised fibular graft has been the treatment options the latter being the preferred one. But the disease being extremely rare not much has been documented about the treatment options. We treated this case by excision of the sclerotic bone ends along with a cuff of periosteum and internal fixation with DCP along with iliac strut graft to restore the length. Successful union was achieved in 3 months and the patient has satisfactory follow-up at 17 months.