The Experts below are selected from a list of 303 Experts worldwide ranked by ideXlab platform

Kevin P. Landolfo - One of the best experts on this subject based on the ideXlab platform.

  • Surgical resection of an intracardiac Rhabdomyoma
    The Annals of Thoracic Surgery, 2000
    Co-Authors: Hartmuth B Bittner, Ajeet D. Sharma, Kevin P. Landolfo
    Abstract:

    There are only a few previous reports of intracardiac Rhabdomyomas causing ventricular arrhythmias and near syncope. In this report we describe the successful surgical resection of an intracardiac Rhabdomyoma using cardiopulmonary bypass, blood cardioplegia, and hypothermia. Preoperative evaluation consisting of echocardiography, computed tomography (CT), magnet resonance imaging (MRI), and positron emission tomography (PET) strongly suggested the presence of a symptomatic primary cardiac tumor projecting from the interventricular septum into the right ventricle.

  • cardiac Rhabdomyoma in an adult patient presenting with ventricular arrhythmia
    Chest, 2000
    Co-Authors: Richard A Krasuski, Kevin P. Landolfo, Aaron Hesselson, Kenneth J Ellington, Thomas M Bashore
    Abstract:

    Cardiac Rhabdomyomasare extremely uncommon in the adult patient. We describe a previouslyhealthy man who presented with ventricular arrhythmias resulting from aright ventricular, cardiac Rhabdomyoma. Echocardiography, CT scanning, and MRI are recognized as useful diagnostic modalities for intracardiaclesions. Cardiac catheterization in our patient demonstrated thepresence of a tumor blush. This has not previously been reported withcardiac Rhabdomyomas. Although lesions may spontaneously regress, surgery is of ten necessary and frequently resolves the underlyingarrhythmia.

Daniel M. Berney - One of the best experts on this subject based on the ideXlab platform.

  • Spermatic cord Rhabdomyoma
    Urology, 2000
    Co-Authors: Pattabiraman Maheshkumar, Daniel M. Berney
    Abstract:

    A 67-year-old man presented with a scrotal swelling. Intraoperatively, this swelling was found to arise from the spermatic cord structures and was completely excised. Histopathology revealed a Rhabdomyoma arising from the cord. The patient has had no evidence of recurrence in the past 24 months. We present the various types of Rhabdomyomas and discuss the differential diagnosis for a spermatic cord swelling.

Colin J Mcmahon - One of the best experts on this subject based on the ideXlab platform.

  • rapid regression of left ventricular outflow tract Rhabdomyoma after sirolimus therapy
    Pediatrics, 2014
    Co-Authors: Colm Breathnach, Jane Pears, Orla Franklin, David Webb, Colin J Mcmahon
    Abstract:

    The neonatal presentation of cardiac Rhabdomyomas varies in severity from severe outflow tract obstruction to minimal cardiac dysfunction. The natural history for these lesions is spontaneous regression in the majority of cases. We describe a newborn boy with severe left ventricular outflow tract obstruction secondary to a large Rhabdomyoma. The tumor infiltrated the paraaortic area and extended around the origin of the right coronary artery, making surgical resection challenging. Oral sirolimus therapy resulted in a rapid regression of the tumor and alleviation of outflow tract obstruction within 1 month of treatment. This is the first report of sirolimus therapy in alleviating critical left ventricular outflow tract obstruction in this condition.

Pattabiraman Maheshkumar - One of the best experts on this subject based on the ideXlab platform.

  • Spermatic cord Rhabdomyoma
    Urology, 2000
    Co-Authors: Pattabiraman Maheshkumar, Daniel M. Berney
    Abstract:

    A 67-year-old man presented with a scrotal swelling. Intraoperatively, this swelling was found to arise from the spermatic cord structures and was completely excised. Histopathology revealed a Rhabdomyoma arising from the cord. The patient has had no evidence of recurrence in the past 24 months. We present the various types of Rhabdomyomas and discuss the differential diagnosis for a spermatic cord swelling.

Giusepe Spriano - One of the best experts on this subject based on the ideXlab platform.

  • Rhabdomyoma of the parapharyngeal space presenting with dysphagia.
    Dysphagia, 2007
    Co-Authors: Barbara Pichi, Valentina Manciocco, Paolo Marchesi, Raul Pellini, P. Ruscito, Antonello Vidiri, Renato Covello, Giusepe Spriano
    Abstract:

    Rhabdomyoma is an exceedingly rare soft tissue benign tumor of skeletal muscle origin classified into cardiac and extracardiac types based on location. Extracardiac Rhabdomyoma is further classified into adult, genital, and fetal type depending on the degree of differentiation. Adult Rhabdomyomas are rare, but morphologically characteristic, benign mesenchymal tumors with mature skeletal muscle differentiation that in 90% of cases arise in the head and neck region, mainly in the mucosa of the oropharynx, nasopharynx, and larynx, from the branchial musculature of third and fourth branchial arches. Most patients are between 40 and 70 years old, with a mean age of 60 years with a male predominance. Usually presenting symptoms include upper airway obstruction, Eustachian tube dysfunction, and mucosal or neck mass, but rarely does it arise as pure dysphagia. This article presents a case of parapharyngeal Rhabdomyoma presenting with only progressive dysphagia.