The Experts below are selected from a list of 21 Experts worldwide ranked by ideXlab platform
C Paolozzi - One of the best experts on this subject based on the ideXlab platform.
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Progressive Rubella Panencephalitis follow up eeg study of a case
Acta neurologica, 1992Co-Authors: A Guizzaro, E Volpe, F Bravaccio, R Cotrufo, C PaolozziAbstract:: Progressive Rubella Panencephalitis is a very rare slow virus disease of the nervous system. The authors present a case, concerning a young man, aged 20 years, died 11 months after the onset of the disease. The following peculiarities of the case are emphasized: 1) the clinical symptomatology and the evolution (myoclonus, lack of cerebellar impairment) could suggest the diagnosis of SSPE; 2) the EEG recordings showed epileptiform abnormalities, long latency diffuse periodic complexes and--during interferon therapy and simultaneously with a temporary clinical improvement--the appearance of short latency anterior periodic complexes.
Clarisse L Dolman - One of the best experts on this subject based on the ideXlab platform.
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Progressive Rubella Panencephalitis clinical course and response to isoprinosine
Developmental Medicine & Child Neurology, 2008Co-Authors: Aubrey J Tingle, G Donald, M Kettyls, William St J Buckler, Clarisse L DolmanAbstract:SUMMARY This report describes the clinical course of a 16-year-old Canadian-born Chinese boy who has Progressive Rubella Panencephalitis. The progression, the lack of response to ‘Isoprenosine’, and the additional finding of myopathy are discussed. The clinical and pathological features of this rare, Progressive neurological disorder are also summarized. In view of the last major Rubella pandemic occuring in the mid-60s, it is likely that during the next few years physicians will diagnose an increased number of patients with this distinct neurological entity. RESUME Panencephalite Progressive rubeoleuse: evolution clinique et reponse a l'lsoprenosine Cet article decrit levolution clinique d'une panencephalite Progressive rubeoleuse chez un garcon de 16 ans, chinois, ne au Canada. L'teolution, l'absence de reponse a l'lsoprenosine et les symptomes additionnels de myopathic frappant la musculature des extremites sont discutes. Les caracteristiques cliniques et pathologiques de ce trouble neurologique rare sont aussi detaillees. Du fait de la derniere pandemie majeure de la rubeole dans les annees 1960 et les epidemies ulterieures, il est vraissemblable qu'un nombre accru de malades presentant ce syndrome neurologique distinct sera rencontre dans les prochaines annees. ZUSAMMENFASSUNG Progrediente RbtelnPanencephalitis: Klinischer Verlauf und Reaktion auf Isoprenosin Dieser Fallbericht beschreibt den klininischen Verlauf bei einem 16 Jahre alten, in Canada geborenen chinesischen Jungen mit progredienter RotelnPanencephalitis. Es wird diskutiert uber das Fortschreiten der Krankheit, das Versagen der Isoprensin Therapie und den zusatzlichen Befund einer proximalen Myopathic Die klinischen und pathologischen Merkmale dieser seltenen neurologischen Erkrankung werden ausfuhrlich be-schrieben. Im Hinblick auf die letzte grose Rotelnpandemie in der Mitte der 60ger Jahre und die fortlaufenden Epidemien besteht die Wahrscheinlichkeit, das in den nachsten Jahren zunehmend Patienten mit diesem umschriebenen neurologischen Krankheitsbild diagnostiziert werden. RESUMEN Encefalitis rubeolica progresiva: curso clinico y respuesta a la isoprenosina El caso tratado describe el curso clinico de un nino de raza china nacido en Canada, de 16 anos de edad con una panencefalitis progresiva rubeolica. La progresion, la falta de respuesta a la isoprenosina, el hallazgo adicional de una miopatia que afectaba la musculatura proximal, fue motivo de discusion. Se detallen tambien las characteristicas clinicas y patologicas de esta rara enfermedad neurologica. En vista de la ultima pandemia rubeolica importante a mediados de 1960 y las epidemias que han aparecido posterior-mente, es logico pensar que en los proximos pocos anos sean diagnosticados un numero mayor de pacientes con esta entidad neurologica tan characteristica.
A Guizzaro - One of the best experts on this subject based on the ideXlab platform.
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Progressive Rubella Panencephalitis follow up eeg study of a case
Acta neurologica, 1992Co-Authors: A Guizzaro, E Volpe, F Bravaccio, R Cotrufo, C PaolozziAbstract:: Progressive Rubella Panencephalitis is a very rare slow virus disease of the nervous system. The authors present a case, concerning a young man, aged 20 years, died 11 months after the onset of the disease. The following peculiarities of the case are emphasized: 1) the clinical symptomatology and the evolution (myoclonus, lack of cerebellar impairment) could suggest the diagnosis of SSPE; 2) the EEG recordings showed epileptiform abnormalities, long latency diffuse periodic complexes and--during interferon therapy and simultaneously with a temporary clinical improvement--the appearance of short latency anterior periodic complexes.
Aubrey J Tingle - One of the best experts on this subject based on the ideXlab platform.
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Progressive Rubella Panencephalitis clinical course and response to isoprinosine
Developmental Medicine & Child Neurology, 2008Co-Authors: Aubrey J Tingle, G Donald, M Kettyls, William St J Buckler, Clarisse L DolmanAbstract:SUMMARY This report describes the clinical course of a 16-year-old Canadian-born Chinese boy who has Progressive Rubella Panencephalitis. The progression, the lack of response to ‘Isoprenosine’, and the additional finding of myopathy are discussed. The clinical and pathological features of this rare, Progressive neurological disorder are also summarized. In view of the last major Rubella pandemic occuring in the mid-60s, it is likely that during the next few years physicians will diagnose an increased number of patients with this distinct neurological entity. RESUME Panencephalite Progressive rubeoleuse: evolution clinique et reponse a l'lsoprenosine Cet article decrit levolution clinique d'une panencephalite Progressive rubeoleuse chez un garcon de 16 ans, chinois, ne au Canada. L'teolution, l'absence de reponse a l'lsoprenosine et les symptomes additionnels de myopathic frappant la musculature des extremites sont discutes. Les caracteristiques cliniques et pathologiques de ce trouble neurologique rare sont aussi detaillees. Du fait de la derniere pandemie majeure de la rubeole dans les annees 1960 et les epidemies ulterieures, il est vraissemblable qu'un nombre accru de malades presentant ce syndrome neurologique distinct sera rencontre dans les prochaines annees. ZUSAMMENFASSUNG Progrediente RbtelnPanencephalitis: Klinischer Verlauf und Reaktion auf Isoprenosin Dieser Fallbericht beschreibt den klininischen Verlauf bei einem 16 Jahre alten, in Canada geborenen chinesischen Jungen mit progredienter RotelnPanencephalitis. Es wird diskutiert uber das Fortschreiten der Krankheit, das Versagen der Isoprensin Therapie und den zusatzlichen Befund einer proximalen Myopathic Die klinischen und pathologischen Merkmale dieser seltenen neurologischen Erkrankung werden ausfuhrlich be-schrieben. Im Hinblick auf die letzte grose Rotelnpandemie in der Mitte der 60ger Jahre und die fortlaufenden Epidemien besteht die Wahrscheinlichkeit, das in den nachsten Jahren zunehmend Patienten mit diesem umschriebenen neurologischen Krankheitsbild diagnostiziert werden. RESUMEN Encefalitis rubeolica progresiva: curso clinico y respuesta a la isoprenosina El caso tratado describe el curso clinico de un nino de raza china nacido en Canada, de 16 anos de edad con una panencefalitis progresiva rubeolica. La progresion, la falta de respuesta a la isoprenosina, el hallazgo adicional de una miopatia que afectaba la musculatura proximal, fue motivo de discusion. Se detallen tambien las characteristicas clinicas y patologicas de esta rara enfermedad neurologica. En vista de la ultima pandemia rubeolica importante a mediados de 1960 y las epidemias que han aparecido posterior-mente, es logico pensar que en los proximos pocos anos sean diagnosticados un numero mayor de pacientes con esta entidad neurologica tan characteristica.
R Cotrufo - One of the best experts on this subject based on the ideXlab platform.
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Progressive Rubella Panencephalitis follow up eeg study of a case
Acta neurologica, 1992Co-Authors: A Guizzaro, E Volpe, F Bravaccio, R Cotrufo, C PaolozziAbstract:: Progressive Rubella Panencephalitis is a very rare slow virus disease of the nervous system. The authors present a case, concerning a young man, aged 20 years, died 11 months after the onset of the disease. The following peculiarities of the case are emphasized: 1) the clinical symptomatology and the evolution (myoclonus, lack of cerebellar impairment) could suggest the diagnosis of SSPE; 2) the EEG recordings showed epileptiform abnormalities, long latency diffuse periodic complexes and--during interferon therapy and simultaneously with a temporary clinical improvement--the appearance of short latency anterior periodic complexes.